Case Report

A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements

Table 1

Laboratory data.

Complete blood count
 WBC (μL) 3200 
 Seg (%)43.0
 Lym (%)38.0
 Mono (%) 18.0
 Eos (%) 1.0
 RBC (×104/μL)393
 Hb (g/dL)11.9
 Ht (%)34.7
 Plt (×104/μL)12.5
Urine
 Sugar(−)
 Protein (±)
 (g/day)0.56
 OB(2+)
 WBC(−)
Chemistry
 TP (g/dL)11.1
 Albumin (%)23.0
α1 (%)2.4
α2 (%)4.5
β (%)3.0
γ (%)67.1
 M protein(−)
 T.Bil (mg/dL)0.3
 AST (U/L)19
 ALT (U/L)9
 LDH (U/L)146
 ALP (U/L)194
γ-GTP (U/L)14
 ChE (U/L)162
 KL-6 (U/mL)117
 CK (U/L)12
 BUN (mg/dL)21.6
 Cr (mg/dL)1.27
 UA (mg/dL)7.1
 AMY (mEq/L)103
 Na (mEq/L)133
 K (mEq/L)4.5
 Cl (mEq/L)102
 Ca (mg/dL)8.4
 P (mg/dL)3.9
Coagulation
 PT-INR (INR)1.10
 APTT (sec)27.2
 Fib (mg/dL)317.0
 D-dimer (μg/mL)0.86
Immunology
 CRP (mg/dL)0.65
 ESR (1 h) (mm)74
 Anti-CCP Ab (IU/mL)1.8>
 RF (mg/dL)1>
 C3 (mg/dL)18.7
 C4 (mg/dL)0.9
 CH50 (U/mL)4.7>
 IgG (mg/dL)7838.1
 IgG4 (mg/dL)2750
 IgA (mg/dL)108.6
 IgM (mg/dL)193.3
 sIL-2R (U/mL)3562
 HBsAg(−)
 HBcAb (S/CO)0.16
 HCVAb(−)
 Anti-dsDNA Ab(−)
 Anti-U1-RNP Ab(−)
 Anti-Sm Ab(−)
 Anti-nuclear Ab 1280 ×
 Homogeneous1280 ×
 Speckled40> ×
 Nucleolar40> ×
 Centromere40> ×
 Peripheral40> ×
 Plasma type(−)
β2-GPI Ab (U/mL)1.3>
 LAC1.0
 Anticardiolipin IgG (U/mL)7

CRP: C-reactive protein; ESR: erythrocyte sedimentation rate; sIL-2R: soluble interleukin-2 receptor; β2-GPI Ab: β2-glycoprotein I antibody; LAC: lupus anticoagulant.