Case Report
A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements
| Complete blood count | | WBC (μL) | 3200 | Seg (%) | 43.0 | Lym (%) | 38.0 | Mono (%) | 18.0 | Eos (%) | 1.0 | RBC (×104/μL) | 393 | Hb (g/dL) | 11.9 | Ht (%) | 34.7 | Plt (×104/μL) | 12.5 | Urine | | Sugar | (−) | Protein | (±) | (g/day) | 0.56 | OB | (2+) | WBC | (−) | Chemistry | | TP (g/dL) | 11.1 | Albumin (%) | 23.0 | α1 (%) | 2.4 | α2 (%) | 4.5 | β (%) | 3.0 | γ (%) | 67.1 | M protein | (−) | T.Bil (mg/dL) | 0.3 | AST (U/L) | 19 | ALT (U/L) | 9 | LDH (U/L) | 146 | ALP (U/L) | 194 | γ-GTP (U/L) | 14 | ChE (U/L) | 162 | KL-6 (U/mL) | 117 | CK (U/L) | 12 | BUN (mg/dL) | 21.6 | Cr (mg/dL) | 1.27 | UA (mg/dL) | 7.1 | AMY (mEq/L) | 103 | Na (mEq/L) | 133 | K (mEq/L) | 4.5 | Cl (mEq/L) | 102 | Ca (mg/dL) | 8.4 | P (mg/dL) | 3.9 | Coagulation | | PT-INR (INR) | 1.10 | APTT (sec) | 27.2 | Fib (mg/dL) | 317.0 | D-dimer (μg/mL) | 0.86 | Immunology | | CRP (mg/dL) | 0.65 | ESR (1 h) (mm) | 74 | Anti-CCP Ab (IU/mL) | 1.8> | RF (mg/dL) | 1> | C3 (mg/dL) | 18.7 | C4 (mg/dL) | 0.9 | CH50 (U/mL) | 4.7> | IgG (mg/dL) | 7838.1 | IgG4 (mg/dL) | 2750 | IgA (mg/dL) | 108.6 | IgM (mg/dL) | 193.3 | sIL-2R (U/mL) | 3562 | HBsAg | (−) | HBcAb (S/CO) | 0.16 | HCVAb | (−) | Anti-dsDNA Ab | (−) | Anti-U1-RNP Ab | (−) | Anti-Sm Ab | (−) | Anti-nuclear Ab |
1280 × | Homogeneous | 1280 × | Speckled | 40> × | Nucleolar | 40> × | Centromere | 40> × | Peripheral | 40> × | Plasma type | (−) | β2-GPI Ab (U/mL) | 1.3> | LAC | 1.0 | Anticardiolipin IgG (U/mL) | 7 |
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CRP: C-reactive protein; ESR: erythrocyte sedimentation rate; sIL-2R: soluble interleukin-2 receptor; β2-GPI Ab: β2-glycoprotein I antibody; LAC: lupus anticoagulant.
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