A Case of Familial Mediterranean Fever with Extensive Lymphadenopathy and Complex Heterozygous Genotype Presenting in the Fourth Decade

Table 1

Review of literature of lymphadenopathy in familial Mediterranean fever.

Anatomical region	Number of cases	Reference
Abdominal	13	[25, 27–29, 31, 32]
Retroperitoneal^†	5	[25–28]
Thoracic (hilar and paratracheal)^†	2	[25]
Peripheral (cervical and axillary)	2	[25, 30]
Pelvic/inguinal^†	0	—

^†Anatomic region where lymphadenopathy was identified in the current report.