| | Diagnostic studies and workup | Treatment | Outcome | Case report | Gender | Age | Pertinent history | Signs & symptoms at presentation | Other manifestations of autoimmune disease | CXR | ECG | Labs | Initial ECHO (EF%) | Steroid | AZA | CYP | Plasmapheresis/IVIG | Clinical | ECHO (EF%) |
| Ashrafi, 2011 | M | 35 | None | 3 months progressive SOB, lower edema swelling | Myositis | DCM | NSR with nonsustained VT | Anti-Ro, anti-La, ANA (1 : 640) | 16 | Y | N | N | Y | Worsening | Not reported |
| Baquero, 2011 | F | 22 | FH: CREST | DOE, JVD, lower extremity edema | Lupus nephritis | Bilateral pleural effusions | Sinus tachycardia with nonspecific T wave changes | ESR 71, ANA (1:64), ds-DNA, anti-Smith, low C3, C4 | 15 | Y | N | Y | N | Improved | 60% |
| Sandrasegaran, 1991 | F | 42 | None | Fever x 1 week | None | Congestion, white-out | Mild ST depressions in anterior-lateral leads | Anemia, ESR 150; ANA + (1 : 100); lupus anticoagulant, low C3/C4, anti-Ro | Severe, no EF% | Y | N | N | N | Improved | Reported as improved; no number given |
| Frustaci, 1996 | M | 38 | None | Fever, palpitations, SOB, weakness x 2 week | Mucosal ulcers | Mod pulmonary congestion | Diffuse ST-T abnormalities | Anemia, ESR 120; | 45 | Y | N | N | N | None given | 65% |
| Routray, 2004 | F | 36 | None | Dyspnea, orthopnea, tachycardia | None | Pulmonary congestion, left pleural effusion | Diffuse ST-T abnormalities | ESR 80; ANA + (1 : 40); anti-ds-DNA + | 35 | Y | N | N | N | Improved | 45%, 10 day follow-up |
| Hoang, 2015 | F | 26 | None | Cough, dyspnea, weight loss x 1 month | None | Bilateral lower lobe patchy infiltrates | None | Anemia, AKI, anti-Ro, | 35 | Y | N | N | N | Improved | 60% |
| Woo, 2009 | F | 27 | None | Dyspnea, orthopnea x 2 weeks | Lupus nephritis | Cardiomegaly, interstitial pulmonary edema | None | Anemia; ESR 33; ANA +; low C3/C4; ds-DNA+, anti-La | 30 | Y | N | Y, 1 da y | N | Improved | 55% |
| Usalan, 2007 | F | 32 | None | Palpitations, malaise, dyspnea, orthopnea x 10 days | Lupus nephritis, hemolysis | Cardiomegaly, pulmonary congestion bilaterally | Sinus tachycardia with nonspecific ST-T wave changes | Anemia, ESR 90, hemolysis (Coombs direct +), ANA (1 : 160), ds-DNA, low C3/C4, anti-cardiolipin | 24 | Y | N | N | N | Improved | 55% |
| van der Laan- Baalbergen, 2009 | F | 19 | Arthralgias | Pancytopenia, fever | Proteinuria | Cardiomegaly, pleural effusion | None | Anemia, ANA, ds-DNA, anti-Smith, anti-cardiolipin, low C3/C4 | Hypokinesis, pericardial effusion, EF 25% | Y | | N | Y | Y | Improved | F | 40 | DVT | Dyspnea, alopecia, rash, weakness progressing to cardiogenic shock | Renal Bx: lupus nephritis | Not reported | None | ANA, ds-DNA, Jo, Sm, SSA, SSB, ENA, aCL, cardiac biopsy positive | 23 | Y | Y | Y | N | Improved | 55% |
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