Case Report

Primary Neuroendocrine Tumor of the Left Hepatic Duct: A Case Report with Review of the Literature

Table 1

Showing study of reported cases of Biliary tract NET.

No.Case referenceAgeSexComplaintLocation

(1)Pilz, [4] 1961 55FWeaknessCBD
(2) Little et al., [5] 196841FRUQ pain, jaundice,Hilar
(3) Bergdahl, [6] 197679FAutopsy findingDistal CBD
(4) Judge et al., [7] 1976 19MJaundice, painHilar
(5) Gerlock and Muhletaler [8] 197932MJaundiceCBD
(6) Vitaux et al., [9] 198124MJaundiceDistal CBD
(7) Nakamuara et al. [10] 198158FJaundiceCBD
(8) Abe et al., [11] 1983 64MRUQ painCBD
(9) Goodman et al., [12] 198428FRUQ PainCystic duct
(10) Jutte et al., [13] 1986 62MBack PainCHD
(11) Nicolescu and Popescu, [14] 1986 50FRUQ painCBD
(12) Alexander et al., [15] 1986 64FHematemesisCBD
(13) Gastinger et al. [16] 198765FJaundice, PainHilar
(14) Reinhardt et al. [17] 198871FJaundice, feverCBD
(15)Chittal and Ra, [18] 198946FRUQ painCystic duct
(16)Fujita et al., [19] 198955FRUQ painCBD
(17)Bickerstaff and Ross [20] 198957FJaundiceCBD
(18)Brown et al., [21] 199035FJaundiceHilar
(19)Bumin et al., [22] 1990 38FJaundiceCBD
(20) Fellows et al. [23] 199030MJaundiceCBD
(21) Besznyák et al. [24]13FJaundiceHilar
(22)Angeles-Angeles et al., [25] 1991 39FJaundiceCBD
(23)Barron-Rodriguez et al., [26] 1991 36MJaundice, RUQ painCBD
(24) Newman et al., 1992 [27]15FN/ACBD
(25) Dixon et al., 1992 [28]60FRUQ painCBD
(26)Rugge et al., [29] 1992 64FJaundice, RUQ painCysticduct, CBD
(27)Gembala et al., [30] 199328MJaundiceHilar
(28)Mandujano-Vera et al., [31] 1995 53FJaundiceCBD
(29) Sankary et al., [32] 199547FJaundiceHilar
(30) Hao et al., [33] 1996 47MIncidental findingCBD
(31) Kopelman et al., [34] 1996 44MJaundiceCBD
(32) Belli et al., [35] 1996 CBD78MJaundiceCBD
(33) Bembenek et al., [36] 199812FJaundiceHilar
(34) Nahas et al., [37] 199861FJaundiceHilar
(35) Ross et al., [38] 1999 65FJaundiceCBD
(36) Chamberlain and Blumgart [39] 199937FItchingHilar
(37) Chamberlain and Blumgart [39] 199967FItchingHilar
(38) Hermina et al., [40] 199969MRUQ painCystic duct
(39) Perakath et al. [42] 199936FJaundice, PainCHD
(40)Chan et al [41] 200014MJaundiceHilar
(41)Maitra et al., [42] 200053FJaundice,CBD
(42)Maitra et al., [42] 200061FJaundice, itchingHilar
(43)Juturi et al., [43] 200043MJaundice, itchingCBD
(44)Turrión et al., [44] 200251FJaundice, itchingHilar
(45)Pawlik et al., [45] 200359MJaundiceHilar
(46)Podnos et al., [46] 200365FCholecystitisCBD
(47)Podnos et al., [46] 200327MJaundice, itchingCBD
(48)Volpe et al., [47] 200319MJaundice, painCBD
(49)Menezes et al., [48]30MJaundiceCHD
(50)Ligato et al., [49] 200533FIrritable bowelHilar
(51)Hubert et al., [50] 2005NAMJaundiceCBD
(52)Hubert et al., [50] 2005NAMJaundiceCBD
(53)Hubert et al., [50] 2005NAFJaundiceCBD
(54) Nesi et al., [51] 2006 30MJaundice, iarrhoeaCBD
(55) Kim et al., [52] 200667FJaundiceCBD
(56) Caglikulekci et al., [53] 200640FJaundiceHilar
(57)Honda et al., [54] 200676MJaundice, painCBD
(58)Todorki et al., [55] 200773MJaundice, FeverCBD
(59)Sethi et al., [56] 200751MERCP findingCHD with Cystic
(60)Stavridi et al., [57] 2007NANANACystic duct
(61)Jiménez et al., [58] 200760MJaundiceHilar
(62)Ferrone et al., [59] 2007NANANANA
(63)Nafidi et al., [60] 200831FRUQ painCBD
(64)Gusani et al., [61] 2008NANANACBD
(65)Schmitt et al., [62] 2008NANANAHilar
(66)Costantini et al., [63] 2008NANANACHD
(67)Felekouras et al., [64] 200960FJaundiceCystic duct
(68)Price et al., [65] 2009NANAJaundiceCBD
(69)Price et al., [65] 2009NANAJaundiceCBD
(70)Price et al., [65] 2009NANAJaundiceHilar
(71)Tonnhofer et al., [66]6FJaundiceCBD
(72)Zhan et al. [67] 201010MNACBD
(73)Squillaci et al., [68] 201052MJaundiceCBD
(74)Squillaci et al., [68] 201070MJaundiceCBD
(75)Tsalis et al., [69] 201077MIncidentalHilar
(76)Lee et al., [70] 201159MJaundiceCBD
(77)Athanasopoulos et al., [71] 201143MJaundiceCBD
(78)Present case69FPainLeft hepatic duct

CHD: common hepatic duct, CBD: common bile duct, Hilar at the common bile duct bifurcation.