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Case Reports in Surgery
Volume 2013 (2013), Article ID 469201, 6 pages
http://dx.doi.org/10.1155/2013/469201
Case Report

Epithelioid Hemangioendothelioma of the Mastoid: Resection for Recurrence and Adjuvant Radiation with 8-Year Followup

1Department of Neurosurgery, Cedars-Sinai Medical Center, Los Angeles, CA 90048, USA
2Division of Neurosurgery, The Neurosciences Institute, Albany Medical Center, Albany, NY 12208, USA
3Department of Pathology, Albany Medical Center, Albany, NY 12208, USA

Received 14 November 2012; Accepted 5 December 2012

Academic Editors: K. Honma and G. Rallis

Copyright © 2013 Doniel Drazin et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Epithelioid hemangioendothelioma (EH) is a rare, vascular neoplasm that can affect any age group and has been reported previously in sites including bone, liver, lung, breast, and brain. We describe a case of EH located in the mastoid, which appears to be the first report of EH in this site. The patient was 62 years old when they presented with dizziness and nausea. A suboccipital surgical approach was utilized to resect the tumor. After 18-month followup, the patient was symptom-free; however, imaging demonstrated a recurrence and the patient was taken back to the operating room for a resection. There is no evidence of recurrence after 8 years of followup. This paper aims to reinforce the need for a timely radical excision and aggressive clinical followup as the best hope for cure. Here, we describe an illustrative case and review the pertinent literature.