Canadian Respiratory Journal

Canadian Respiratory Journal / 2002 / Article

Case Report | Open Access

Volume 9 |Article ID 958921 |

John K Reid, Henrike Rees, Donald Cockcroft, "Long-Term Survival in a Patient with Pulmonary Lymphangioleiomyomatosis", Canadian Respiratory Journal, vol. 9, Article ID 958921, 5 pages, 2002.

Long-Term Survival in a Patient with Pulmonary Lymphangioleiomyomatosis


A patient with pulmonary lymphangioleiomyomatosis was diagnosed more than 22 years after the onset of symptoms by a thoracoscopic lung biopsy, after a high resolution computerized tomogram of the chest was highly suggestive of the disease. After nearly 30 years since the onset of her symptoms, the patient leads a relatively normal life with only mildly abnormal lung function and has minimal reduction in her exercise tolerance. There have been few reports of patients surviving for such a long time after the onset of this disease; the literature suggests that most patients die within 15 years of symptom onset.

Copyright © 2002 Hindawi Publishing Corporation. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

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