Research Article

Poorer Prognosis of Idiopathic Pleuroparenchymal Fibroelastosis Compared with Idiopathic Pulmonary Fibrosis in Advanced Stage

Table 4

Outcomes and events during the follow-up period.

IPPFEIPF value
()()

Outcome
 Alive1838
 Dead1129
 CauseNS
  Chronic respiratory failure411
  Acute exacerbation412
  Lung cancer01
  Others35

Events
 Pneumothorax/ pneumomediastinum194<0.01
 Recurrent infection23NS

TreatmentNS
 Oral corticosteroids917
 Immunosuppressant drugs213
 Pirfenidone1031
 Home oxygen therapy626