Research Article
Poorer Prognosis of Idiopathic Pleuroparenchymal Fibroelastosis Compared with Idiopathic Pulmonary Fibrosis in Advanced Stage
Table 4
Outcomes and events during the follow-up period.
| | IPPFE | IPF | value | () | () |
| Outcome | | | | Alive | 18 | 38 | | Dead | 11 | 29 | | Cause | | | NS | Chronic respiratory failure | 4 | 11 | | Acute exacerbation | 4 | 12 | | Lung cancer | 0 | 1 | | Others | 3 | 5 | |
| Events | | | | Pneumothorax/ pneumomediastinum | 19 | 4 | <0.01 | Recurrent infection | 2 | 3 | NS |
| Treatment | | | NS | Oral corticosteroids | 9 | 17 | | Immunosuppressant drugs | 2 | 13 | | Pirfenidone | 10 | 31 | | Home oxygen therapy | 6 | 26 | |
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