Assessment of Respiratory Function and Need for Noninvasive Ventilation in a Cohort of Patients with Myotonic Dystrophy Type 1 Followed at One Single Expert Center

Table 1

Demographic and clinical features of the whole cohort (n = 151).

Age	43.00 [34.00–52.00]
Sex, n (%)
Male	67 (44.4)
Female	84 (55.6)
MIRS, n (%)
1	9 (6)
2	36 (23.8)
3	50 (33.1)
4	52 (34.4)
5	4 (2.7)
Disease duration	13.00 [6.00–19.00]
BMI	24.82 [21.71–27.51]
CTG	600 [400–920]
Sitters, n (%)	4 (2.7)
PM/ICD, n (%)	16 (10.6)

All data are presented as median and interquartile ranges, except where otherwise indicated. Patients were classified as “sitters” if unable to walk for 10 meters without support. MIRS, Muscle Impairment Rating Scale; BMI, Body Mass Index; PM, pacemaker; ICD, implantable cardiac defibrillator.