Echocardiographic Features of Cardiomyopathy in Emery-Dreifuss Muscular Dystrophy

Table 2

Cardiac chamber diameters and volumes of EDMD patients and healthy controls.

	EDMD1 patients, n = 29	EDMD2 patients, n = 12	Healthy controls, n = 25	value, EDMD1 versus EDMD2	value, EDMD versus control
LVEDdi (mm/m2)	29.3 (26.8–32.0)	32.0 (29.9–33.2)	25.5 (23.5–27.6)	0.26	<0.001
LVEDVi (ml/m2)	71.9 (53.7–92.4)	63.2 (56.2–86.2)	48.2 (43.0–51.9)	0.83	<0.001
LVESdi (mm/m2)	19.1 (15.4–23.1)	20.3 (16.6–22.1)	15.7 (14.3–17.9)	0.70	<0.001
LVESVi (ml/m2)	35.1 (24.0–45.6)	30.8 (22.9–48.4)	16.6 (14.1–18.9)	0.90	<0.001
RVdi (mm/m2)	12.8 (11.3–15.5)	14.4 (12.4–18.1)	12.9 (12.5–14.3)	0.18	0.37
LAdi (mm/m2)	20.7 (19.2–22.7)	23.4 (20.1–24.6)	18.4 (17.8–20.0)	0.07	<0.001
LAVi (ml/m2)	34.6 (26.9–39.6)	35.9 (24.9–39.2)	24.4 (20.7–26.4)	0.81	<0.001
RAVi (ml/m2)	41.6 (28.6–76.7)	35.9 (28.5–47.9)	19.6 (17.8–22.9)	0.53	<0.001

LAdi: left atrium dimension index; LAVi: left atrial volume index; LVEDdi: left ventricular end-diastolic dimension index; LVEDVi: left ventricular end-diastolic volume index; LVESdi: left ventricular end-systolic dimension index; LVESVi: left ventricular end-systolic volume index; RAVi: right atrial volume index; RVdi: right ventricular dimension index.