Research Article
Serum Level of D-Lactate in Patients with Cystic Fibrosis: Preliminary Data
Table 1
Clinical characteristics and diet composition of 43 patients with cystic fibrosis. Diet composition was expressed as median and 1–3 quartiles.
| | Values |
| | Age (years) | 7.8 (range: 6 months–18 years) | | Sex: female/male (n/n) | 19/19 | | Mutation (n (%)) | | | delF508del/delF508del | 22 (57.8) | | delF508del/other | 13 (34.0) | | Other | 3 (7.9) | | Schwachman-Kulczycki score (pts) | 74.2 (range 45–110) | | Clinical features (n (%)) | | | Pancreatic insufficiency | 29 (76.3) | | Malnutrition (BMI < 3 pcn) | 18 (47.4) | | Symptoms from respiratory tract/recurrent respiratory tract infection | 23 (60.5) | | Liver dysfunction | 7 (18.4) | | History of meconium ileus/treated surgically | 3 (7.9)/1 (2.6) | | Salt-loss syndrome | 2 (5.2) | | Elevated concentration of faecal calprotectin | 16 (42.1) | | Diet composition | | | Energy (kcal/kg body mass) | 70.7 (55.8–90.4) | | Protein (g/kg body mass) | 2.4 (1.8–3.3) | | Carbohydrates (g/kg body mass) | 8.5 (6.8–10.6) | | Fat (g/kg body mass) | 1.9 (1.6–3.7) | | Dietary support | | | PEG | 2 (5.2%) | | Nasogastric tube | 3 (7.8%) | | Orally high caloric formula | 25 (65.78%) |
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