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Gastroenterology Research and Practice
Volume 2009 (2009), Article ID 282753, 3 pages
http://dx.doi.org/10.1155/2009/282753
Case Report

Megacystis-Microcolon-Intestinal Hypoperistalsis Syndrome: A Case Report

1Department of Pediatric Surgery, Yuzuncu Yil University, 65100 Van, Turkey
2Department of Pediatry, Yuzuncu Yil University, 65100 Van, Turkey

Received 10 March 2009; Accepted 14 July 2009

Academic Editor: Ronnie Fass

Copyright © 2009 Mehmet Melek et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Megacystis Microcolon Intestinal Hypoperistalsis Syndrom (MMIHS) is a quite rare congenital and fatal disease which was firstly defined by Berdon and his colleagues. It appears through a widely enlarged bladder and microcolon and its cause is unknown (Berdon et al., 1976; Carmelo et al., 2005; Makhija et al., 1999; Loening-Baucke and Kimura 1999; Redman et al., 1984; Hsu et al., 2003; Yigit et al., 1996; Srikanth et al., 1993). The disease is found in females three or four times more than in males (Srikanth et al., 1993; Sen et al., 1993; Hirato et al., 2003). Most of the cases die within the early months of their lives (Yigit et al., 1996; Srikanth et al., 1993; Sen et al., 1993; Hirato et al., 2003). We present the case of a female newborn with antenatal ultrasound revealing intestinal mass and bilateral hydroureteronephrosis. The case was admitted for intestinal obstruction after birth.