Research Article

The Pattern of Juvenile Idiopathic Arthritis in a Single Tertiary Center in Saudi Arabia

Table 1

The ILAR classification of JIA.

Systemic arthritisArthritis with, or preceded by, daily fever of at least 2-week duration that is documented to be daily for at least 3 days and accompanied by one or more of the following: (i) evanescent, nonfixed, erythematous rash; (ii) generalized lymph node enlargement; (iii) hepatomegaly and/or splenomegaly; (iv) serositis  
Exclusion criteria: A, B, C, and D

OligoarthritisArthritis in 1–4 joints during the first 6 months of disease.  
Two subtypes: (i) persistent oligoarthritis affects no more than four joints throughout the disease course; 
(ii) extended oligoarthritis affects a total of more than four joints after the first 6 months of disease 
Exclusion criteria: A, B, C, D, and E

Polyarthritis (RF-negative) Arthritis affecting 5 or more joints during the first 6 months of disease: tests for RF are negative 
Exclusion criteria: A, B, C, D, and E

Polyarthritis (RF-positive) Arthritis in 5 or more joints during the first 6 months of disease: tests for RF are positive  
Exclusion criteria: A, B, C, and E

Psoriatic arthritis Arthritis plus psoriasis  or  arthritis plus at least two of the following: dactylitis, nail pitting, or onycholysis, psoriasis in a first-degree relative 
Exclusion criteria: B, C, D, and E

Enthesitis-related arthritis Arthritis plus enthesitis  or  arthritis or enthesitis, plus at least two of the following: presence of or a history of sacroiliac joint tenderness and/or inflammatory lumbosacral pain, presence of HLA-B27 antigen, onset of arthritis in a male over 6 years of age, acute (symptomatic) anterior uveitis, history of AS, ERA, sacroiliitis with IBD, reactive arthritis, or acute anterior uveitis in a first-degree relative 
Exclusions criteria: A, D, and E

Undifferentiated arthritis Arthritis that do not fulfill criteria in any of the above categories or fulfills criteria in two or more of the above categories

Exclusion criteria: A: Psoriasis in the patient or a first-degree relative, B: Arthritis in an HLA-B27-positive male with arthritis onset after 6 years of age, C: Ankylosing spondylitis, enthesitis-related arthritis, sacroiliitis with inflammatory bowel disease, Reiter’s syndrome, or acute anterior uveitis in a first-degree relative, D: Presence of IgM rheumatoid factor on at least two occasions for at least 3 months apart, E: Presence of systemic arthritis.
Adapted from © The Journal of Rheumatology Publishing, 2001. All rights reserved. Petty et al. [1].