Cochlear Implantation in Patients with Neurofibromatosis Type 2 and Patients with Vestibular Schwannoma in the Only Hearing Ear

Table 1

Series report on cochlear implantation and vestibular schwannoma resection regardless on the approach used or timing between surgeries.

Author

Patients no.

Age

Approach

Radiation

Time to implantation (m)

Cause HL

Followup (m)

Cochlear implant PTA dB

Speech tests

Telephone

Daily use

EPT after VS resection (m)

Arístegui and Denia [28] 2005

1

52

TL

No

S

NF2

18

NA

VI 80%, BWR 90%, daily words 100%, CID 100%.

Yes

NA

NA

2

45

TL

No

S

VS

6

NA

VI 100%, BWR 95%, daily words 100%, CID 100%

NA

NA

+

1

35

NA

No

NA

NF2

28

55

0% all speech tests

NA

Yes

NA

2

51

NA

No

NA

NF2

40

35

MTSr 6%, MTSc 79%

NA

Yes

NA

Lustig et al. [9] 2006

3

16

NA

No

NA

NF2

30

40

0% all speech tests

NA

Yes

NA

4

28

NA

No

NA

NF2

88

45

0% all speech tests

NA

Yes

NA

5

57

NA

No

NA

NF2

9

30

Phonemes 35%, HINT 21%

NA

Yes

NA

1

15

MF

No

9

NF2

156

NA

3SWLOS 45%, 3SWLCS 75%

Yes

NA

EPS 6 m +

2

26

RS

No

2

NF2

108

NA

HINT 91%, CID 98%, CUNY45%

Yes

NA

EPS 2 m +

Neff et al. [8] 2007

3

53

RS

No

72

NF2

60

NA

HINT 96%, CID 100%, CUNY 93%, 4CS 100%

Yes

NA

EPS 12 m +

4

37

RS

No

Few m

NF2

98.4

NA

HINT 83%, CID 90%, 4CS 100%

Yes

NA

EPS 2 m +

5

37

TL

No

S

NF2

61.2

NA

HINT 96%, CID 100%, 4CS 100%

Yes

NA

NA

6

31

RS

No

1.5

NF2

84

NA

CID 22%, 4CS 85%, CUNY 0%

No

NA

EPS 1.5 m +

1

47

RS

No

3

NF2

12

NA

VI 100%, CI 100%, BWR 80%, SR 90%, CPC

Yes

Yes

EPS +

Vincenti et al. [29] 2008

2

24

TL

No

S

NF2

12

NA

100% VI 100%, CI 100%, BWR 72%, SR 81%, CPC 86%

Yes

Yes

CNAP, S +

3

32

TL

No

3

NF2

12

NA

VI 100%, CI 100%, BWR 50%, SR 50%, CPC 55%

Yes

Yes

EPS +

4

36

RS

No

3

NF2

12

NA

VI 40%, CI 39%, BWR 10%, SR 0%, CPC 0%

No

Yes

CNAP−

Tran Ba Huy et al. [30] 2009

1

41

RS

No

4

NF2

24

NA

OSWSLR 90%, OSWSWLR 68%, OSSLR 89%, OSSWLR 81%, OSSWLRWN 6%, PCC 89%, PWCC 30%

Yes

NA

EPS 2 m +

2

17

TL

No

S

NF2

12

NA

OSWSLR 97%, OSWSWLR 87%, OSSLR 99%, OSSWLR 97.8%, PCC 89%, PWCC 60%

Yes

NA

NA

TL: translabyrinthine; NA: nonavailable; MF:middle fossa; RS: retrosigmoid; S: simultaneous; NF2: neurofibromatosis type 2; VS: vestibular schwannoma; 3SWLOS: three syllabic word list open set; 3SWLCS: 3 syllabic word list closed set; HINT: hearing in noise sentence testing; CID: Central Institute for the Deaf sentences of everyday speech; CUNY: City University of New York sentences in noise; 4CS: four-choice spondee (closed set); MTSr: Monosyllable Trochee Spondee recognition; MTSc: Monosyllable Trochee Spondee category; SDS: speech discrimination score; VI: vowel identification; CI: consonant identification; BWR: bisyllable word recognition; SR: sentence recognition; CPC: common phrases comprehension; OSWSLR: open-set word score with lip reading; OSWSWLR: open set word score without lip reading; OSSLR: open set sentences with lip reading; OSSWLR: open set sentences without lip reading; OSSWLRWN: open-set sentences without lip reading with noise; PCC: phone with contextual cues; PWCC: phone without contextual cues; EPT: electrical promontory test; EPS: electrical promontory stimulation; CNAP: compound action potential. Bold letters: patients who initially had negative promontory stimulation.