Long-Term Effect of Enzyme Replacement Therapy with Fabry Disease

Table 1

Grades of severity of hearing loss. In Japan, the severity of SSNHL has been classified as follows.

Grade 1	Less than 40 dB
Grade 2	More than 40 dB, less than 60 dB
Grade 3	More than 60 dB, less than 90 dB
Grade 4	90 dB or more