Vasculitis in Systemic Sclerosis

Table 4

Characteristics of eleven cases of AAV in SSc.

Characteristic	Number (%)
Sex (M/F)	4/7 (36%/64%)
Age (mean ± SD)	53 ± 14 (range from 19 to 71)
SSc duration (mean ± SD in yrs); 9 pts	4.49 ± 3.37 (range from 0.42 to 10 yrs)
SSc Dx to AAV dx (mean ± SD in yrs); 10 pts	3.85 ± 2.67 (range from 0.42 to 8 yrs)
SSc type (Diffuse/Limited)	7/3 (64%/27%)
D-penicillamine use	4 (36%)
Renal involvement	9 (82%) all with crescentic GN on Bx
Pulmonary involvement	2 (18%)
ANA + (>1∶320)	8 (88%)
Scl-70 +	5 (45%)
Anticentromere +	1 (9%)
MPO +	10 (91%)
PR3 +	0