Review Article

IgG4-Related Lymphadenopathy

Table 1

Histological subtypes of IgG4-related lymphadenopathy.

Histological typeDistribution of IgG4+ plasma cellsLymphadenopathy

IMulticentric Castleman’s disease-likeInterfollicularSystemic
IIReactive follicular hyperplasia-likeInterfollicularLocalized
IIIInterfollicular expansion and immunoblastosisInterfollicularSystemic
IVPTGC-typeIntragerminal centerLocalized/systemic
VInflammatory pseudotumor (IPT-) likeInterfollicularLocalized

PTGC; progressively transformed germinal centers.