Review Article
IgG4-Related Lymphadenopathy
Table 1
Histological subtypes of IgG4-related lymphadenopathy.
| | Histological type | Distribution of IgG4+ plasma cells | Lymphadenopathy |
| I | Multicentric Castleman’s disease-like | Interfollicular | Systemic | II | Reactive follicular hyperplasia-like | Interfollicular | Localized | III | Interfollicular expansion and immunoblastosis | Interfollicular | Systemic | IV | PTGC-type | Intragerminal center | Localized/systemic | V | Inflammatory pseudotumor (IPT-) like | Interfollicular | Localized |
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PTGC; progressively transformed germinal centers.
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