Review Article

Knitting the Threads of Silk through Time: Behçet’s Disease—Past, Present, and Future

Table 1

The worldwide prevalence of BD.

Country/area
Study (year)Patients ()Population/ participantsPrevalence
(per 100,000)

Northern Europe
 UK (Yorkshire)Chamberlain (1977) [5]325,000,0000.64
 Scotland Jankowski et al. (1992) [6]155,500,0000.3
 Ireland (Dublin) Kilmartin et al. (1997) [7]241,058,2642.27
 Sweden (Skane) Mohammad et al. (2013) [8]40809,3174.94
Europe
 Germany Papoutsis et al. (2006) [9]1653,391,3444.87
 France (Paris) Mahr et al. (2008) [10]791,094,4127.1
 Italy (Rome) Valesini et al. (1991) [11]155NA19
 Greece Kaklamani et al. (2000) [12]90NA11
Mediterranean
 Turkey
  Tokat Baş et al. (2016) [13]142,325602
  Kayseri Çölgeçen et al. (2015) [14]95,218170
  Havsa Cakir et al. (2004) [15]14,86120
  Istanbul Azizlerli et al. (2003) [16]10123,986420
  Ankara Idil et al. (2002) [17]1617,256110
  Ordu Yurdakul et al. (1988) [18]195,121370
  Istanbul Demirhindi et al. (1981) [19]44,94080
Mediterranean
 Iran Davatchi et al. (2007) [20]710,29168
 Egypt Assaad-Khalil et al. (1997) [21]274NA16
 Jordan Madanat et al. (2000) [22]200NA27
Others
 US (Olmsted County) Calamia et al. (2009) [23]13144,2485.2
 Japan Nakae et al. (1993) [24]3316NA13.5
 Korea Bang et al. (2011) [25]15,554NA30.2
 China Zhang et al. (2006) [26]1996NA14