Research Article

Telerehabilitation Using Fitness Application in Patients with Severe Cystic Fibrosis Awaiting Lung Transplant: A Pilot Study

Table 1

Patient demographics and baseline clinical characteristics.

CharacteristicHome PR ()Outpatient hospital PR () value

Age, years30 (10)29 (7)0.12
Female5 (46%)8 (100%)0.01
BMI, kg/m219.7 (5.4)20.0 (5.8)0.71
FeV1 (L).88 (.49).95 (.51)0.84
FeV1 (% predicted)26 (6)29 (14)0.28
O2 requirements during exercise, L/min2 (4)1 (4)0.78
Pre 6-minute walk test, meters412 (106)394 (130)0.81
Pre UCSD dyspnea43 (34)58 (45), 0.77
GSE27 (10), NA
IPAQ165 (784)NA

Medians and (interquartile range). BMI: body mass index; FeV1: forced expiratory volume during 1 second; UCSD: University of California San Diego (Shortness of Breath Questionnaire); PR: pulmonary rehabilitation, GSE: General Self-Efficacy Questionnaire; IPAQ: International Physical Activity Questionnaire.