Table of Contents
ISRN Surgery
Volume 2011 (2011), Article ID 106487, 4 pages
http://dx.doi.org/10.5402/2011/106487
Case Report

Living Donor Liver Transplantation for Caroli's Disease: A Report of Two Cases

Liver Transplantation Unit, Bonsucesso Federal Hospital, Health Ministry, Rio de Janeiro, 21041-030, RJ, Brazil

Received 20 February 2011; Accepted 24 March 2011

Academic Editors: U. Cioffi, B. Clements, J. J. Diaz, and P. M. N. Y. H. Go

Copyright © 2011 Klaus Steinbrück et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Caroli's disease (CD) is a rare autosomal recessive disorder characterized by intrahepatic cystic dilatation of the bile ducts. Patients with bilobar or progressive disease may require orthotopic liver transplantation (OLT). In the MELD era, living donor liver transplantation (LDLT) raised as the ultimate treatment option for these patients, once their MELD score is usually low. Herein, we describe 2 cases of patients (a 2-year-old girl and a 19-year-old teenager) that successfully underwent LDLT as a treatment for diffuse CD. The good postoperative courses of the two cases indicate that LDLT is a feasible option in the treatment of this disorder, even in complicated or early age patients.