|
| Authors | Journal (year) | Affiliation (province) | Number family | BCS patients | Age (years) | Clinical presentation | Type of BCS |
|
| Wang et al. | Curr Probl Surg (1996) EN | Beijing Post and Telecommunication Hospital (Beijing) | 1st family | Two brothers | NA | NA | IVC webs |
| | | 2nd family | Twin sisters | NA | NA | MOVC |
|
|
Sun et al. |
Gan Dan Wai Ke Za Zhi (1997) CN |
No. 89 Hospital of Chinese PLA (Shandong) |
3rd family |
Two brothers (farmers) | 24 | Abdominal distension, swelling of lower limbs (4 yrs), ascites, hepatomegaly, varicosity of abdominal wall and lower limbs | IVC stenosis with MHV obstruction |
| 26 | Abdominal distension and swelling of lower limbs (6 yrs), ascites, hepatomegaly, splenomegaly, varicosity of abdominal wall and lower limbs | IVC stenosis with MHV obstruction |
|
Liu et al.;
Wang et al. |
Zhonghua Xiao Hua Za Zhi (1999); The 7th Chinese National Congress of Gastroenterology (2007); Wei Chang Bing Xue (2007) CN |
Departments of Digestive Diseases and Interventional Radiology, General Hospital of Chinese PLA (Beijing) |
4th family |
An elder brother and a younger sister | 29 | Abdominal distension (20 days), oliguria and swelling of lower limbs (4 days), gross ascites, hepatomegaly, varicosity of chest and abdominal wall | Three HVs obstruction |
| 25 | Abdominal distension (2 months); hepatomegaly, ascites | Three HVs obstruction with IVC stenosis |
| 5th family | Two brothers | NA | Hepatomegaly | HV obstruction |
|
|
Liu et al. |
Lin Chuang Xiao Hua Bing Za Zhi (2000) CN |
Second People's Hospital of Anyang City (Henan) |
6th family | Father and an elder son | NA | NA | NA |
|
7th family | An elder brother and a younger sister | NA | NA | NA |
|
|
Feng et al. |
Zhonghua Yi Xue Za Zhi (2000); Zhonghua Xue Ye Xue Za Zhi (2000); Zhonghua Fang She Za Zhi (2001) CN |
Department of Radiology, First Affiliated Hospital of China Medical University (Liaoning) |
8th family |
Four sisters | 40* | Brachypnea (15 yrs), abdominal distension and swelling of lower limbs (10 yrs), varicosity of abdominal wall and lower limbs | SOVC |
| 28* | Swelling of lower limbs (5 yrs), varicosity of chest and abdominal wall and lower limbs, hepatomegaly | MOVC |
| 35* | Asymptomatic | IVC stenosis |
| 23 | Asymptomatic | IVC stenosis with two HVs stenosis |
|
9th family |
Two sisters | 43 | Swelling of lower limbs (4 yrs), ascites, varicosity of abdominal wall and lower limbs | SOVC with IVC thrombosis |
| 33* | Abdominal distension and swelling of lower limbs (5 yrs), varicosity of chest and abdominal wall, hepatomegaly | MOVC |
|
| Wang et al. |
Guang Dong Yi Xue Za Zhi (2000); Shi Yong Yi Xue Za Zhi (2001); Zhongguo Xian Dai Yi Xue Za Zhi (2001); Lin Chuang Gan Dan Bing Za Zhi (2005) CN |
Department of Digestive Diseases, Second Affiliated Hospital of Ji'nan University (Guangdong) | 10th family | An elder brother and a younger sister | 50 | Recurrent variceal bleeding (30 yrs), abdominal distension, hepatomegaly, no ascites | SOVC |
| 43 | Abdominal distension (1 yr); normal liver and spleen, no ascites | MOVC |
|
Yuan et al.;
Qin et al. | Hua Bei Mei Tan Yi Xue Yuan Xue Bao (2002); Zhongguo Pu Tong Wai Ke Za Zhi (2002) CN | Department of General Surgery, First Affiliated Hospital of Xinxiang Medical College (Henan) | 11th family | An elder sister and a younger sister | NA | Asymptomatic, esophageal varices | MOVC |
|
|
Zhao et al. |
Zhonghua Xiao Hua Za Zhi (2003) CN |
Hospital of Chenggu County (Shaanxi) |
12th family |
An elder sister
and a younger brother | 36 | Abdominal distension and swelling of lower limbs (8 yrs), varicosity of chest and abdominal wall, splenomegaly, normal liver, no ascites | IVC obstruction |
| 31 | Abdominal distension (0.5 yr), massive variceal bleeding (4 days), edema of both lower limbs, varicosity of chest and abdominal wall and lower limbs, splenomegaly, normal liver, moderate ascites | IVC stenosis |
|
Zheng et al.;
Lin et al. |
Zhengzhou Da Xue Xue Bao (2005); Zhonghua Pu Tong Wai Ke Za Zhi (2006) CN |
Department of General Surgery, First Affiliated Hospital, Zhengzhou University (Henan) | 13th family | An elder sister and a younger brother | NA | NA | NA |
| 14th family | Twin sisters | NA | NA | NA |
|
