Research Article

BPI-ANCA and Long-Term Prognosis among 46 Adult CF Patients: A Prospective 10-Year Follow-Up Study

Table 2

PsA colonization, BPI-ANCA, and outcome. Adult CF-patients divided into groups based on Leeds classification and IgA BPI-ANCA levels at baseline and subsequent endpoints during followup.

Leeds classificationLeeds I + IILeeds IIILeeds IV
BPI-ANCA levelBPI−BPI+BPI++BPI−BPI+BPI++BPI−BPI+BPI++

Inclusion ( )51296**1165*1
5 years % with endpoint016.7%33.3% 16.7% 00020% 0
( with endpoint)(2)(3)(1)(1*)
10 years % with endpoint033.3%77.8% 33.3% 0100% 020% 0
( with endpoint) (4)(7)(2**)(1)(1*)
Last followup, % with endpoint20%41.7%88.9%33.3%0100%040%0
( with endpoint) (1) (5) (8) (2**) (1) (2*)

Patient with colon cancer.
**Patient with Burkholderia cepacia.