Recent Understanding on Diagnosis and Management of Central Nervous System Vasculitis in Children

Table 2

New classification of childhood vasculitis [2].

Predominantly large vessel vasculitis	Takayasu arteritis
Predominantly medium-sized vessel vasculitis	Childhood polyarteritis nodosa
	Cutaneous polyarteritis
	Kawasaki disease
Predominantly small vessels vasculitis	(A) Granulomatous:
	Wegener’s granulomatosis
	Churg-Strauss syndrome
	(B) Nongranulomatous:
	Microscopic polyangiitis
	Henoch-Schönlein purpura
	Isolated cutaneous leucocytoclastic vasculitis
	Hypocomplementic urticarial vasculitis
Other vasculitis	Behcet disease
	Vasculitis secondary to infection (including hepatitis B associated polyarteritis nodosa), malignancies, and drugs, including hypersensitivity vasculitis
	Vasculitis associated with connective tissue diseases
	Isolated vasculitis of the central nervous system
	Cogan syndrome
	Unclassified