An Update on the Genetics of Usher Syndrome

Table 1

Clinical features of Usher syndrome types.

	USH1	USH2	USH3
Hearing loss	Severe to profound	Moderate to severe	Moderate to severe
	Congenital	Congenital	Progressive
	Stable	Stable
Vestibular function	Altered	Normal	Variable
RP onset	Usually prepubertal	Around pubertyor postpubertal	Around puberty or postpubertal
Language	Unintelligible	Intelligible	Intelligible