Review Article
An Update on the Genetics of Usher Syndrome
Table 1
Clinical features of Usher syndrome types.
| | USH1 | USH2 | USH3 |
| Hearing loss | Severe to profound | Moderate to severe | Moderate to severe | Congenital | Congenital | Progressive | Stable | Stable | |
| Vestibular function | Altered | Normal | Variable | RP onset | Usually prepubertal | Around pubertyor postpubertal | Around puberty or postpubertal | Language | Unintelligible | Intelligible | Intelligible |
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