Review Article

Ischemic Retinal Vasculitis and Its Management

Table 1

Cause of retinal vasculitis according to the type of vessels involved and association with retinal ischemia.

Mainly involve arteriesMainly involve veinsAssociated with retinal ischemia

Infectious disordersAcute retinal necrosis
Toxoplasmosis
Cat scratch disease
West Nile virus
Tuberculous hypersensitivity
Syphilis
CMV
HIV
Rift Valley fever virus
HTLV-1
Tuberculous hypersensitivity
West Nile virus

Noninfectious disordersSLE
APHA
Takayasu’s disease
IRVAN
GPA
Churg-Strauss syndrome
Crohn’s disease
Polyarteritis nodosa
Susac syndrome
Dermatomyositis
Behçet’s disease
Sarcoidosis
Multiple sclerosis
Birdshot chorioretinopathy
APMPPE
Pars planitis
HLAB27 associated uveitis
Behçet’s disease
Sarcoidosis
Multiple sclerosis
SLE
APHA
Takayasu’s disease
IRVAN
GPA
Dermatomyositis
Churg-Strauss syndrome
Crohn’s disease
Polyarteritis nodosa
Susac syndrome
Idiopathic retinal vasculitis

SLE: systemic lopus erythematosus; APHA: antiphospholipid antibody syndrome; IRVAN: idiopathic retinal vasculitis, arteriolar macroaneurysms, and neuroretinitis; CMV: cytomegalovirus; HIV: human immunodeficiency virus; HTLV-1: human T-cell lymphoma virus type 1; APMPPE: acute posterior multifocal placoid pigment epitheliopathy; GPA: granulomatosis with polyangiitis.