Research Article

Spectral Domain Optical Coherence Tomographic Findings of Bietti Crystalline Dystrophy

Table 1

Patients’ characteristics and OCT findings.

Patient
number
Age GenderEyeStage CMT
(μm)
SCT
(μm)
ORTIntraretinal hyperreflective dotsBright plaqueChoroidal hyperreflective dotsVitreomacular interface status

134MOD
OU
2203125 + + ++ VMA
2153131 + + ++ VMA
245MOD
OU
3141140 + + ++
2181108 + + ++
3 33FOD
OU
2194140 + + ++
2198104 + + ++
466MOD
OU
2225 95 + + ++
2100 52 + + ++
566FOD
OU
241 69 + + ++
258 39 + + ++
628MOD
OU
2245210 + + ++
2227179 + + ++
765MOD
OU
3161 22 + VMT
3160 30 + VMT
824MOD
OU
3179 24 +
3274 32 +
945FOD
OU
2160181 + + ++ VMA
2198153 + + ++ VMA
1039MOD
OU
356 29 + + ++
347 31 + + +
1156MOD
OU
2183120 + + ++
2183116 + + ++
1244MOD
OU
2152 66 + + ++
2195 92 + + ++

CMT: central macular thickness, SCT: subfoveal choroidal thickness, VMA: vitreomacular adhesion, VMT: vitreomacular traction, and ORT: outer retinal tabulation.
*Patient number 1 had also bilateral cystoid macular edema [10].