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Patient number | Age at onset/sex | Clinical profile | Duration of disease before IVIg (years) | Therapy before IVIg | Total steroids dose (mg) | Side effects of tx before IVIg | Number of relapses | Number of recurrences | Number of cycles of IVIg | Number of months of IVIg | Staging before IVIg | Staging after IVIg |
| | 1 | 64/F | Mouth, conjunctiva, vagina, skin | 2 | Prednisone 100 mg/day × 24 mo
Azathioprine 150 mg/day × 24 mo
Cyclophosphamide 100 mg/day × 20 mo | 72,000
108,000
60,000 | Osteoporosis, cataract, depression, anemia, leukopenia | 0 | 3 | 20 | 18 | RE: 3
LE: 3 | RE: 3
LE: 3 | | 2 | 58/F | Mouth, conjunctiva, nose, skin | 3 | Prednisone 90 mg/day × 36 mo
Azathioprine 100 mg/day × 35 mo
Cyclosporine (topical treatment)
Methylprednisolone (topical treatment) | 97,200
105,000 | Anemia, leukopenia, Cushing syndrome | 3 | 4 | 10 | 8 | RE: 2
LE: 2 | RE: 1
LE: 1 | | 3 | 72/F | Mouth, conjunctiva, vagina | 4 | Prednisone 90 mg/day × 36 mo
Cyclophosphamide 100 mg/day × 20 mo | 97,200
60,000 | Diabetes mellitus, hypertension | 0 | 1 | 18 | 18 | RE: 2
LE: 2 | RE: 2
LE: 1 | | 4 | 65/M | Mouth, conjunctiva | 7 | Prednisone 90 mg/day × 9 mo
Azathioprine 100 mg/day × 7 mo
Dapsone 75 mg/day × 60 mo | 24,300
21,000
135,000 | None | 1 | 0 | 14 | 14 | RE: 3
LE: 3 | RE: 3
LE: 3 | | 5 | 80/M | Mouth, conjunctiva | 3 | Prednisone 80 mg/day × 9 mo
Azathioprine 150 mg/day × 6 mo
Dapsone 75 mg/day × 12 mo | 21,600
27,000
27,000 | None | 0 | 0 | 20 | 17 | RE: 3
LE: 3 | RE: 3
LE: 3 | | 6 | 78/M | Mouth, conjunctiva, glans penis | 10 | Prednisone 80 mg/day × 20 mo
Azathioprine 100 mg/day × 6 mo
Cyclosporine (topical treatment) | 48,000
18,000 | Diabetes mellitus, leukopenia, hypertension | 2 | 1 | 19 | 19 | RE: 3
LE: 3 | RE: 3
LE: 3 |
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