Figure 2: Explanted heart of a 31-year-old patient with failing Fontan. (a) Macroscopic view of the explanted heart, showing the tricuspid atresia (TA) with hypoplastic right ventricle (RV), grossly dilated right atrium (RA) and left ventricle with septal hypertrophy. (b) and (c) show histologic cuts of the right ventricular myocardium with areas of interstitial myocardial fibrosis (arrow) and areas of marked endomyocardial fibroelastosis (arrow head).