Review Article

Are Onconeural Antibodies a Clinical Phenomenology in Paraneoplastic Limbic Encephalitis?

Table 1

Classification of paraneoplastic neurological syndromes.

Central nervous system
 Limbic encephalitis
 Encephalomyelitis
 Brainstem encephalitis
 Stiff-person syndrome
 Opsoclonus-myoclonus
 Subacute cerebellar degeneration
 Paraneoplastic visual syndromes
  Cancer-associated retinopathy
  Melanoma-associated retinopathy
  Paraneoplastic optic neuropathy
 Motor neuron syndromes
  Subacute motor neuronopathy
  Other motor neuron syndromes

Peripheral nervous system
 Acute sensorimotor neuropathy
 Subacute sensory neuronopathy
 Chronic sensorimotor neuropathy
 Subacute autonomic neuropathy
 Paraneoplastic peripheral nerve vasculitis

Neuromuscular junction and muscle
 Myasthenia gravis
 Lambert-Eaton syndrome
 Polymyositis/dermatomyositis
 Acute necrotizing myopathy
 Cachectic myopathy
 Neuromyotonia