Review Article

Are Onconeural Antibodies a Clinical Phenomenology in Paraneoplastic Limbic Encephalitis?

Table 3

Differential diagnoses of limbic encephalitis.

Infectious disorders
 Herpes simplex virus encephalitis
 Neurosyphilis
 Progressive multifocal leukoencephalopathy
 Rabies
 Creutzfeldt-Jakob disease

Metabolic disorders
 Metabolic encephalopathy (uremic, hepatic, Cushing
 syndrome, etc.)
 Wernicke-Korsakoff syndrome
 Hashimoto’s encephalopathy

Systemic autoimmune disorders
 Sjögren syndrome
 Systemic lupus erythematosus
 Antiphospholipid syndrome

Malignancies
 Lymphoma
 Glioma
 Gliomatosis cerebri

Degenerative disorders
 Alzheimer’s disease
 Lewy-body dementia
 Frontotemporal dementia

Others
 Stroke with posterior cerebral artery involvement
 Central nervous system vasculitis
 Temporal lobe epilepsy
 Nonconvulsive status epilepticus
 Transient global amnesia
 Acute demyelinating encephalomyelitis
 Posterior reversible encephalopathy syndrome
 Intoxication (alcohol, lithium, etc.)
 Alcohol withdrawal syndrome
 Psychiatric disorder