Review Article

Histopathological Evaluation of Behçet's Disease and Identification of New Skin Lesions

Table 1

Diagnostic criteria of Behçet’s disease defined by International Study Group.

Mucocutaneous lesionsDescription

Recurrent oral ulcerationMinor, aphthous, major aphthous, or herpetiform ulceration observed by physician or patient that recurred at least 3 times in one 12-month period

Plus 2 of the following criteria:
Recurrent genital ulcerationAphthous ulceration or scarring observed by physician or patient
Eye lesionsAnterior uveitis, posterior uveitis, cells in vitreous on slit lamp examination, or retinal vasculitis observed by ophthalmologist
Cutaneous lesionsErythema nodosum, pseudofolliculitis, papulopustular lesions, or acneiform nodules observed by physician in postadolescent patients not receiving corticosteroid treatment
Positive pathergy testRead by physician at 24 to 48 hours