Primary Cardiac Synovial Sarcoma: A Case Report and Brief Review of the Literature

Boulmay, Brian; Cooper, Gary; Reith, John D.; Marsh, Robert

doi:https://doi.org/10.1155/2007/94797

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Case Report | Open Access

Volume 2007 | Article ID 094797 | https://doi.org/10.1155/2007/94797

Primary Cardiac Synovial Sarcoma: A Case Report and Brief Review of the Literature

Brian Boulmay,¹Gary Cooper,²John D. Reith,³and Robert Marsh¹

Academic Editor: Kees C. Verhoef

Received20 Nov 2006

Accepted18 Apr 2007

Published04 Jul 2007

Abstract

Synovial sarcoma comprises approximately 10% of all soft tissue sarcoma diagnoses; a primary synovial sarcoma of the myocardium is exceedingly rare. There have been very few cases reported in the literature thus far. With the identification of the characteristic and diagnostic chromosomal abnormality t(X;18), this may become an increasingly recognized entity. Our report adds to the limited published cases of primary cardiac synovial sarcoma with the characteristic t(X;18). Further elucidation of the effects of this translocation on the cell cycle may lead to directed therapies in the future.

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Copyright

Copyright © 2007 Brian Boulmay et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

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