Clinical Study
Primary Adult Renal Ewing's Sarcoma: A Rare Entity
Table 1
Treatment and outcome in the seven patients with primary renal Ewing’s sarcoma.
(a) Patients without metastatic disease at presentation |
| Age in years | Year of diagnosis | Sex | Side of renal primary | Radical nephrectomy | chemotherapy | Site of relapse | Disease-free interval in months | Status at last follow up | Survival in months |
| 50 | 1993 | Male | Left | Yes | 4 VID/2 IE | No relapse | 149.7 | Alive (no disease) | 149.7 | 34 | 2000 | Male | Right | Yes | 3 CVD/3 EP | Lung | 55.4 | Alive (stable disease) | 107.4 | 57 | 2007 | Female | Left | Yes | 1 VAC | Liver, spleen | 5.3 | Died (progressive disease) | 6.5 | 43 | 2007 | Male | Left | Yes | 4MVAC > 2VIDE > 3VAD | Bone | 5.1 | Alive (stable disease) | 15.6 |
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(b) Patients with metastatic disease at presentation |
| Age in years | Year of diagnosis | Sex | Side of renal primary | Radical nephrectomy | Metastatic site at presentation | chemotherapy | Time to disease progression in months | Status at last follow up | Survival in months |
| 35 | 1997 | Female | Left | No | Liver, node | 3 PD/3ID | 24 | Died (progressive disease) | 62.8 | 32 | 1999 | Female | Right | No | Liver, node | Etoposide | 0 | Died (progressive disease) | 26.5 | 50 | 2007 | Male | Left | No | Liver, adrenal | 4VIDE > 6VAC | 12 | Died (progressive disease) | 13.1 |
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Abbreviations: V: vincristine (vinblastine in MVAC), P: cisplatin, I: ifosfamide, D: doxorubicin, E: etoposide, A: actinomycin D (doxorubicin in IVAD).
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