Guidelines

Guidelines for the Management of Soft Tissue Sarcomas

Table 4

Soft tissue sarcomas grouped by chemosensitivity.

Relative chemosensitivityExamples of soft tissue sarcomas

Chemotherapy integral to management(i) Ewing’s sarcoma family tumours
(ii) Embryonal and alveolar rhabdomyosarcoma

Chemosensitive(i) Synovial sarcoma
(ii) Myxoid/round cell liposarcoma
(iii) Uterine leiomyosarcoma

Moderately chemosensitive(i) Pleomorphic liposarcoma
(ii) Myxofibrosarcoma
(iii) Epithelioid sarcoma
(iv) Pleomorphic rhabdomyosarcoma
(v) Leiomyosarcoma
(vi) Malignant peripheral nerve sheath tumour
(vii) Angiosarcoma
(viii) Desmoplastic small round cell tumour
(ix) Scalp and face angiosarcoma

Relatively chemo-insensitive(i) Dedifferentiated liposarcoma
(ii) Clear cell sarcoma
(iii) Endometrial stromal sarcoma

Chemoinsensitive(i) Alveolar soft part sarcoma
(ii) Extraskeletal myxoid chondrosarcoma