Extra-Abdominal Desmoid Tumors Associated with Familial Adenomatous Polyposis

Table 2

Extracolonic FAP manifestation (Neiuwenhuis [33] and Groen [54]).

Extracolonic manifestation	Prevalence in FAP patients
CHRPE	70–75%
Osteomas and dental abnormalities	70–90%
Upper GI tumors	50–90%
Epidermoid cysts and lipomas	25–50%
Desmoid tumors	15–20%
Adrenal tumors	7–13%
Papillary thyroid cancer	1-2%
Hepatoblastoma	1-2%
Brain Tumors (Medulloblastoma and others)	1-2%
Pancreatic Cancer	1%