SARC006: Phase II Trial of Chemotherapy in Sporadic and Neurofibromatosis Type 1 Associated Chemotherapy-Naive Malignant Peripheral Nerve Sheath Tumors

Table 2

Baseline NF1 clinical findings in 34 patients with NF1 MPNST.

NF1 diagnostic signs (number of subjects with data provided)
6 or more CAL ()	17
Intertriginous freckling ()	19
Neurofibromas ()	26
Subcutaneous neurofibromas (); (0/1–9/≥10)	4/10/10
Cutaneous neurofibromas (); (0/1–9/≥10)	6/5/13
Plexiform neurofibroma ()	12
Paraspinal neurofibromas ()	12
Glioma/optic glioma ()	1/1
Other morbidity
Scoliosis ()	5
Intellectual delay ()	8
Hypertension ()	8