Sarcoma / 2017 / Article / Tab 2

Clinical Study

SARC006: Phase II Trial of Chemotherapy in Sporadic and Neurofibromatosis Type 1 Associated Chemotherapy-Naive Malignant Peripheral Nerve Sheath Tumors

Table 2

Baseline NF1 clinical findings in 34 patients with NF1 MPNST.

NF1 diagnostic signs (number of subjects with data provided)
 6 or more CAL ()17
 Intertriginous freckling ()19
 Neurofibromas ()26
 Subcutaneous neurofibromas ()
(0/1–9/≥10)
4/10/10
 Cutaneous neurofibromas ()
(0/1–9/≥10)
6/5/13
 Plexiform neurofibroma ()12
 Paraspinal neurofibromas ()12
 Glioma/optic glioma ()1/1
Other morbidity
 Scoliosis ()5
 Intellectual delay ()8
 Hypertension ()8

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