Review Article

High-Dose Chemotherapy with Stem Cell Rescue in Desmoplastic Small Round Cell Tumor: A Single-Institution Experience and Review of the Literature

Table 1

Patients with desmoplastic small round cell tumor treated at Children’s Hospital at Montefiore.

PatientAge at diagnosisGenderDate of diagnosisDate of relapseDate of last follow-upStatus at last follow-upMonths to last follow-up1st treatment2nd treatment3rd treatment4th treatment5th treatment

116Female5/8/200812/8/2015Alive, disease free91OophorectomyP6 chemotherapySurgery at MSKCCSCTTotal abdominal radiation
221Male9/24/20126/1/20159/24/2016Alive, relapsed40Resection of abdominal tumorP6 chemotherapySurgery at MSKCCSCTPartial course of radiation
311Male11/16/201011/16/2015Alive, disease free60Vincristine, dactinomycin, cyclophosphamideTumor resectionSCTRadiation
419Male1/9/20089/28/20094/27/2011Death from metastatic disease39P6 chemotherapyTumor resectionSCTRadiation

MSKCC: Memorial Sloan Kettering Cancer Center; SCT: stem cell transplant.