The Disease Burden of Hereditary Angioedema: Insights from a Survey in French-Canadians from Quebec
Table 1
Demographics and clinical characteristics.
Characteristic
Full sample (n = 35), median (min, max) or n (%)
Age (years)
46 (16, 73)
Sex
Male
7 (20%)
Female
28 (80%)
Marital status
Common-law
9 (26%)
Married
16 (46%)
Single
10 (29%)
Employed
19 (54%)
HAE type
Type I
16 (46%)
Type II
1 (3%)
HAE nC1-INH
15 (43%)
Unknown
3 (9%)
Age at first HAE symptoms (years)†
16 (1, 69)
Age at HAE diagnosis (years)
34 (2, 69)
Diagnostic delay (years)‡
10 (0, 44)
Diagnosing doctor
Internist
6 (17%)
Immunologist/allergist
26 (74%)
Gastroenterologist
1 (3%)
Hematologist/oncologist
1 (3%)
Dermatologist
1 (3%)
Family screening
All
1 (3%)
Only some members
20 (57%)
No
13 (37%)
Do not know/NA
1 (3%)
Family deaths due to HAE
4 (11%)
HAE, hereditary angioedema; HAE nC1-INH, HAE with normal C1 inhibitor; NA, not applicable. †One participant did not respond to this question (n = 34). ‡Two participants were excluded from the calculation as one respondent with HAE nC1-INH did not report their age at first symptom, and another participant with HAE type I identified as having received their diagnosis prior to experiencing their first symptom (n = 33).