Review Article

Rett Syndrome: Coming to Terms with Treatment

Table 2

Rett syndrome timing of regression period.

Age at regression Classic RTTVariant RTT
Higher functioningLower functioning

<6 months13 (1.7%)3 (4.4%)27 (38%)
6–<12 months54 (7.0%)2 (2.9%)9 (12%)
12–<18 months281 (36%)2 (2.9%)15 (21%)
18–30 months351 (46%)26 (38%)10 (14%)
>30 months74 (9.6%)35 (52%)11 (15%)

Total7736872