Research Article
Non-Hodgkin Lymphoma in Children with Primary Immunodeficiencies: Clinical Manifestations, Diagnosis, and Management, Belarusian Experience
Table 1
Characteristics of patients with NHLa.
| Characteristic | Patients with PIDb, (%) | Immunocompetent patients, (%) |
| Sex | | | M | 10 (62.5) | 220 (79.2) | F | 6 (37.5) | 57 (20.8) | Age | | | 0–4 | 6 (37.5) | 52 (18.8) | 5–9 | 5 (31.25) | 85 (30.7) | 10–14 | 2 (12.5) | 86 (31.0) | ≥15 | 3 (18.75) | 54 (19.5) | Stage | | | I + II | 1 (6.25) | 77 (27.8) | III + IV | 15 (93.75) | 200 (72.2) | Morphology | | | Burkitt | 2 (12.5) | 135 (48.7) | T-lymphoblastic | 3 (18.75) | 52 (18.8) | B-lymphoblastic | 0 | 19 (6.9) | DLBCLc | 6 (37.5) | 16 (5.8) | PMLBCLd | 0 | 14 (5.1) | ALCLe systemic | 2 (12.5) | 33 (11.9) | ALCL cutaneous | 1 (6.25) | 0 | PTCLf | 2 (12.5) | 2 (0.7) | B-NHL, unspecified | 0 | 6 (2.2) | Immunological lineage | | | B | 8 (50.0) | 190 (68.6) | T | 8 (50.0) | 87 (31.4) |
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Non-Hodgkin lymphoma, bprimary immune deficiency disease, cdiffuse large B-cell lymphoma, dprimary mediastinal large B-cell lymphoma, eanaplastic large cell lymphoma, and fperipheral T-cell lymphoma.
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