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Case Reports in Pathology
Volume 2012, Article ID 915408, 4 pages
Case Report

Optic Nerve Hemangioblastoma: A Case Report

1Department of Surgery, Division of Neurosurgery, University of Alabama at Birmingham, Birmingham, AL 35294, USA
2Department of Pathology, Division of Neuropathology, University of Alabama at Birmingham, 1960 6th Avenue South, PD6A 175E, Birmingham, AL 35294, USA
3Department of Ophthalmology, University of Alabama at Birmingham, Birmingham, AL 35294, USA

Received 23 January 2012; Accepted 1 March 2012

Academic Editors: Y. Nagashima and D. Vlachodimitropoulos

Copyright © 2012 Holly Zywicke et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


Hemangioblastomas are World Health Organization (WHO) grade I tumors of uncertain histologic origin. These central nervous system tumors are most often found in the posterior fossa, brainstem, and spinal cord. There are fewer than 20 reported cases of optic nerve hemangioblastomas in the literature. We present a patient with visual decline found to have a mass arising from within the posterior orbital canal that grossly involved the optic nerve sheath. Neuropathologic evaluation showed hemangioblastoma. Although not a common tumor in this location, consideration of hemangioblastoma in the differential diagnosis is important as they can have a more aggressive course than other tumors of this region and have a detrimental effect on visual prognosis.