IgG4-Related Sclerosing Cholangitis Involving the Intrahepatic Bile Ducts Diagnosed with Liver Biopsy

Figure 1

Imaging findings in a patient with IgG4-related sclerosing cholangitis (IgG4-SC). (a) At magnetic resonance imaging, no tumor-like lesions are seen. A benign hepatic cyst is indicated (1). (b) Diffuse and multiple intrahepatic biliary stenoses and dilatations at endoscopic retrograde cholangiography (1). The stenoses are relatively long. In classical primary sclerosing cholangitis (PSC), the stenoses would have been shorter, giving the cholangiogram a more beaded appearance. No complete obstruction of a bile duct is seen, a finding that would have been more characteristic of bile duct carcinoma. 2: occlusive balloon, 3: endoscope, 4: guide wire.

(a)

(b)