An Inguinal Perivascular Epithelioid Cell Tumor Metastatic to the Orbit

Table 1

Classification of PEComas (adapted from Bleeker and Folpe, [5, 6]).

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High risk features

 Size > 5 cm

 Infiltrative growth pattern

 High nuclear grade and cellularity

 Mitotic rate > 1/50 HPF

 Necrosis

 Vascular invasion

Benign

 No high risk features

Uncertain malignant potential

 1 high risk feature including size ≥ 5 cm, nuclear pleomorphism, or multinucleated giant cell

Malignant

 2 or more high risk features

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