Malignant Glandular Triton Tumor Arising in the Radial Nerve with Prolonged Survival: A Case Report and Review of the Literature

Table 1

Reported cases of triton tumor with glandular differentiation.

No.	Authors year [reference]	Age/sex	NF1	Location	Divergent differentiation components in MPNST	Treatment and outcome
1	Després et al. 1973 [5]	38/F	Yes	Sciatic nerve	RMS and benign glands	Surgery; recurred at 13 months; DOD at 19 months
2	Warner et al. 1983 [6]	29/M	Yes	Thigh	RMS and benign glands	Surgery; no follow-up data available
3	Daimaru et al. 1984 [7]	27/F	Yes	Buttock	RMS and benign glands	Surgery; DOD after 4 months
4	Christensen et al. 1988 [8]	NAD	NAD	NAD	RMS and benign glands	NAD
5	Christensen et al. 1988 [8]	NAD	NAD	NAD	RMS, osteosarcoma, and benign glands	NAD
6	Ho and Che 1989 [9]	14/F	Yes	Left sciatic nerve	RMS and benign glands of intestinal type epithelium	Surgical excision of the tumor (); no follow-up data available
7	Wong et al. 1991 [10]	39/M	No	Thorax, overlying T1-T4	RMS and malignant glands	Surgery, radiotherapy, and chemotherapy; recurred at 1 year; DOD at 15 months
8	Rose et al. 1992 [11]	34/M	Yes	Brachial plexus	RMS and glands with moderate nuclear atypia	Surgery, radiotherapy, and chemotherapy; recurred at 14 months; DOD at 18 months
9	Woodruff and Christensen 1993 [12]	20/F	Yes	Right side of neck, associated with plexiform neurofibroma	RMS, chondrosarcoma, osteosarcoma, and benign glands	Subtotal surgical resection; DOD after 3 months
10	Ordonez 1998 [13]	28/M	No	Right lumbar area, overlying L5	RMS and glands lined by a single layer of columnar cells or by multiple layers of cuboidal cells having marked nuclear atypia	Surgery, radiotherapy, and chemotherapy (Adriamycin); DOD after 33 months
11	Karpuz et al. 2000 [14]	52/M	No	Chest wall	RMS and benign glands	Surgery; recurred after 5 years
12	Huang et al. 2003 [15]	24/M	No	Thigh	RMS and malignant glands	Surgery; lung metastasis after 5 months; DOD after 6 months
13	Guo et al. 2012 [16]	79/M	NAD	Thigh	RMS, glands, lipoblasts, and ganglion cells	Surgery, radiotherapy, and chemotherapy; recurred after10 months, without metastasis
14	Thway et al. 2015 [17]	40/M	No	Mediastinum	RMS and benign glands	Surgery; brain metastasis after 15 months; transferred for palliation at 24 months
15	AlAli and Amr 2020 current case	26/M	No	Elbow, radial nerve	RMS and malignant glands	Surgery, radiotherapy, and chemotherapy; no recurrence or metastases for 10 years

Abbreviations: RMS: rhabdomyosarcomatous; DOD: dead of disease; NAD: no available data.