Case Report

Diagnosis and Assessment of Disease Activity in Takayasu Arteritis: A Childhood Case Illustrating the Challenge

Table 2

Differential diagnosis of Takayasu Arteritis.

ClassificationSubtype

Primary inflammatory vasculitidesGiant cell arteritis
Kawasaki disease
Polyarteritis nodosa
Wegener’s granulomatosis disease

Secondary inflammatory vasculitidesRheumatic fever
Sarcoidosis
SLE
Behcet’s disease
Spondyloarthropathies

Noninflammatory vascular diseaseFibromuscular dysplasia
Congenital aortic abnormalities
Inherited connective tissue disorders
Neurofibromatosis

Other
Sepsis
Malignancy
Human immunodeficiency virus
Syphilis
Tuberculosis
Radiation fibrosis