A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements

Figure 5

Clinical course of the patient. After admission in April 2014, renal and inguinal lymph node biopsies were performed. We diagnosed IgG4-RD by clinical findings, high level of IgG4, and histological findings in kidney and inguinal lymph node; then prednisolone (0.6 mg/kg/day) was started as therapy. Swelling of the salivary glands improved rapidly and pancytopenia and renal disorder likewise showed improvement. The high levels of serum IgG and IgG4 and hypocomplementemia all also showed marked improvement. These improvements continued until August 2014. The prednisolone dose could be gradually taped.