Systemic Lupus Erythematosus Presenting with Massive Ascites: A Case of Pseudo-Pseudo Meigs Syndrome

Table 1

Review of the literature of the reported cases of Pseudo-Pseudo Meigs Syndrome.

Article	Demographic	Prior SLE diagnosis	Presenting symptoms	CA-125 level (<35 U/mL)	Ascites fluid characteristics	Initial treatment
Tjalma 2005 [4]	38F	Yes	Dyspnea, abdominal tenderness	887 U/mL	Exudate	Prednisone, azathioprine
Schmitt et al. 2005 [5]	33F	No	Dyspnea, abdominal distention, pedal edema, poor appetite	1239 U/mL–2287 U/mL	Exudate; Cytology negative	Prednisone, mycophenolate mofetil, hydroxychloroquine
Ural et al. 2008 [6]	38F	No	Dyspnea, abdominal distention, rash, skin lesions, alopecia	1229 U/mL	Exudate; SAAG < 1.0; AFB negative	Prednisone, hydroxychloroquine
Bes and Soy 2011 [7]	47F	No	Dyspnea, vomiting, diarrhea	233 U/mL	—	Prednisone (40 mg/day)
Dalvi et al. 2012 [8]	56F	Yes	Abdominal distention, poor appetite, weight loss, cachexia	70.1 U/mL	Exudate; SAAG < 1.0; Cytology negative	Prednisone (1 mg/kg/day)
Bes et al. 2013 [9]	42F	No	Abdominal pain, abdominal distention, pedal edema, vomiting, diarrhea	91.3 U/mL	Exudate; Cytology negative	Methylprednisolone (1 g/d × 3 days)
Lee et al. 2013 [10]	29F	No	Dyspnea, abdominal distention, vomiting	345 U/mL	—	Methylprednisolone (1 g/day × 3 days)
	54F	Yes	Abdominal distention, poor appetite, weight loss, cachexia	344.9 U/mL	SAAG < 1.0; Cytology negative	Methylprednisolone (250 mg/day) Cyclophosphamide (750 mg/day)
McVorran et al. (current case) 2016	40F	No	Dyspnea, abdominal distention, Raynaud’s phenomenon, arthralgia, photosensitivity	307 U/mL	SAAG < 1.0; Cytology negative	Methylprednisolone (1 g/d × 3 days)