Case Report

Erosive Arthritis, Fibromatosis, and Keloids: A Rare Dermatoarthropathy

Table 1

Summary of polyfibromatosis cases with a musculoskeletal component.

Author/year/countryAge (years)/genderFibromatosisKeloidsMusculoskeletal featuresX-ray featuresMRI features

Pierard and Lapiere 1979 [4], Belgium20, maleHand fibromatosis, knuckle pads, and “toughness” of skinNACamptodactyly, tendon calcification, facial hyoplasia, osteolysis, and scoliosisOsteolysis of distal ulna, right ring finger proximal phalanx, and first metacarpalNA

Fenton et al. 1986 [7], United Kingdom48, malePalmar fibromatosis, and Peyronie’s diseaseKeloids of arms, shoulders, and presternal areaHand and foot stiffnessErosions of shoulders, hands, and feetNA

Chen et al. 2006 [5], Australia65, maleProgressive fibrosis and contractures of wrist, elbows, knees, and ankles; linear fibrotic cordsNoneInflammatory pain of wrist, elbows, knees, and anklesErosions of left shoulder, elbows, wrists, hands, and feetNA

Kim et al. 2009 [8], South Korea44, malePalmar and plantar nodules and fibromatosisMultiple keloids of trunk and extremitiesAsymptomaticErosions and osteolysis of handsMultiple hand erosions

Cinotti et al. 2013 [9], Italy53, maleFlexion contractures of wrists, fingers, ankles, and toes; gingival hyperplasia and conjunctival fibrosisMultiple keloidsSevere hand and foot deformities and facial changesOsteolysis of wrists, hands, and toes; ankylosisNA

Albarran et al. 2015 [6], Spain33, malePalmar and plantar nodules, palmar fibromatosis, knee contractures and fibromatosis, and gingival hyperplasiaNoneNAErosion in right footSynovitis and effusions in both knees

Present case 2018, USA23, maleFinger flexion contracturesMultiple keloids of trunk and extremitiesMild foot painErosions of feet; hands without erosionsMultiple erosions and synovitis of feet