| | Case | Age | Gender | CTD | Treatments before SCLS | Symptoms and/or laboratory findings at the onset of SCLS | Anti-SSA antibody | Treatments for SCLS | Outcome |
| | 1 [11] | 25 | F | SS | GC | Abdominal pain, nausea, vomiting pericardial effusion, ascites | Positive | GC and diuretics-IVIG | Remission | | 2 [11] | 43 | M | SS
SSc | D-pen | Weight gain, hemoconcentration hypoalbuminemia | Negative | Diuretics and IVIG | Dead | | 3 [11] | 17 | M | PM | GC, MTX, AZA | Edema of upper limbs and face, hemoconcentration, hypoalbuminemia | Negative | IVIG | Remission | | 4 [11] | 45 | F | SS | None | Oliguria, loss of weight hemoconcentration, hypoalbuminemia | Positive | Transfusion and IVIG | Remission | | 5 [11] | 55 | F | SS | None | Hypovolemic shock hemoconcentration, hypoproteinemia | Positive | Transfusion and GC | Remission | | 6 [12] | 61 | M | SSc | None | Shortness of breath, profuse sweating, leg edema, severe fatigue, and otalgia | NA | High-dose GC and diuretics | Remission | | 7 [13] | 52 | F | SSc | Imatinib mesylate | Facial and lower extremity edema, and elevated alkaline phosphatase | NA | Vasopressor | Dead | | 8 [14] | 7 | M | JDM | GC pulse high-dose GC | Edema of the neck and upper limbs, myalgia, oliguria, and hypotension | NA | IVIG | Remission | | 9 [14] | 13 | M | JDM | GC pulse | Generalized edema, myalgia, oliguria, hypotension, and tachycardia | NA | IVIG | Remission | | 10 [14] | 3 | M | JDM | GC pulse high-dose GC | Edema of the face and neck, oliguria, acute kidney, and respiratory failure | NA | IVIG | Remission | | 11 [15] | 40 | F | SLE | GC CPA, AZA | Nausea, vomiting, and intestinal wall edema at CT scan | NA | Transfusion and IS | Remission | | 12 [15] | 41 | F | SLE | GC HCQ | Nausea, vomiting, and intestinal wall edema at CT scan | Positive | High-dose GC | Remission |
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