Case Report
Successful Treatment of Pulmonary Arterial Hypertension in Systemic Sclerosis with Anticentriole Antibody
Table 1
Peripheral blood examination inday 20 after treatment.
| Blood test (day 20) |
| Urinalysis | | Specific gravity | 1.021 | pH | 6 | Protein | + | Blood | – | Nitrite | – | WBC | – | Bacteria | – | CBC | | WBC | 5,000 mL | Neutrophil | 3,000 mL | Eosinophil | 0 mL | Basophil | 0 mL | Lymphocyte | 1,800 mL | Monocyte | 200 mL | RBC | 4.77 × 106 mL | Hb | 13.5 g/dL | MCV | 89.5 fl | Plt | 212 × 103 mL |
| Coagulation | | PT | 18.7 sec | PT-INR | 2.34 | APTT | 52.9 sec | D-dimer | 0.6 mg/mL | Infection | | T-SPOT | (−) | HBs Ab | (−) | HBs Ag | (−) | HCV Ab | (−) |
| Biochemistry | | T-bil | 1.6 mg/dL | D-bil | 0.1 mg/dL | ALP | 72 U/L | γ − GTP | 33 U/L | AST | 35 U/L | ALT | 34 U/L | LDH | 297 U/L | BUN | 10 mg/dL | Cre | 0.55 mg/dL | UA | 4.4 mg/dL | TP | 6.4 g/dL | Alb | 4 g/dL | Pre-Alb | 15 mg/dL | Na | 142 mEq/L | K | 3.7 mEq/L | Cl | 107 mEq/L | Ca | 8.4 mg/dL | IP | 3.6 mg/dL | TG | 101 mg/dL | TC | 122 mg/dL | LDL-C | 69 mg/dL | CPK | 112 U/L | CK-MB | 21 U/L | Glucose | 98 mg/dL | Hb-A1c (NGSP) | 6.2% | CRP | 0.07 mg/dL | Hp | ≦3.0 mg/dL | Ferritin | 69.8 ng/mL |
| Endocrine | | FT4 | 1.17 ng/dL | TSH | 6.33 mgIU/mL | FT3 | 2.69 pg/mL | BNP | 432.1 pg/mL |
| Immune system | | IgG | 1001 mg/dL | IgA | 228 mg/dL | IgM | 94 mg/dL | ANA | ≦40 | C3 | 90 mg/dL | C4 | 21.8 mg/dL | CH50 | 46.9 U/mL | Anti-dsDNA Ab | ≦10I U/mL | Anti-RNP Ab | ≦5.0 U/mL | Anti-Sm Ab | ≦5.0 U/mL | Anti-SS-A/Ro Ab | ≦5.0 U/mL | Anti-SS-B/La Ab | ≦5.0 U/mL | Anti-Scl 70 Ab | ≦5.0 U/mL | Anti-centromere Ab | ≦5.0 U/mL | Anti-CL.β2GPI Ab | ≦1.3 U/mL | Anti-CALG Ab | ≦1.0 U/mL | LAC | ≦1.0 U/mL | PR3-ANCA | ≦1.0I U/mL | MPO-ANCA | ≦1.0 U/mL | RF | ≦5.0 U/mL | Anti-CCP Ab | ≦0.5 U/mL | Anti-ARS Ab | 10 U/mL | Anti-RNA polymerase III Ab | 15.2 |
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