Successful Treatment of Pulmonary Arterial Hypertension in Systemic Sclerosis with Anticentriole Antibody

Table 1

Peripheral blood examination inday 20 after treatment.

Blood test (day 20)
Urinalysis
Specific gravity	1.021
pH	6
Protein	+
Blood	–
Nitrite	–
WBC	–
Bacteria	–
CBC
WBC	5,000 mL
Neutrophil	3,000 mL
Eosinophil	0 mL
Basophil	0 mL
Lymphocyte	1,800 mL
Monocyte	200 mL
RBC	4.77 × 10^6 mL
Hb	13.5 g/dL
MCV	89.5 fl
Plt	212 × 10^3 mL
Coagulation
PT	18.7 sec
PT-INR	2.34
APTT	52.9 sec
D-dimer	0.6 mg/mL
Infection
T-SPOT	(−)
HBs Ab	(−)
HBs Ag	(−)
HCV Ab	(−)
Biochemistry
T-bil	1.6 mg/dL
D-bil	0.1 mg/dL
ALP	72 U/L
γ − GTP	33 U/L
AST	35 U/L
ALT	34 U/L
LDH	297 U/L
BUN	10 mg/dL
Cre	0.55 mg/dL
UA	4.4 mg/dL
TP	6.4 g/dL
Alb	4 g/dL
Pre-Alb	15 mg/dL
Na	142 mEq/L
K	3.7 mEq/L
Cl	107 mEq/L
Ca	8.4 mg/dL
IP	3.6 mg/dL
TG	101 mg/dL
TC	122 mg/dL
LDL-C	69 mg/dL
CPK	112 U/L
CK-MB	21 U/L
Glucose	98 mg/dL
Hb-A1c (NGSP)	6.2%
CRP	0.07 mg/dL
Hp	≦3.0 mg/dL
Ferritin	69.8 ng/mL
Endocrine
FT4	1.17 ng/dL
TSH	6.33 mgIU/mL
FT3	2.69 pg/mL
BNP	432.1 pg/mL
Immune system
IgG	1001 mg/dL
IgA	228 mg/dL
IgM	94 mg/dL
ANA	≦40
C3	90 mg/dL
C4	21.8 mg/dL
CH50	46.9 U/mL
Anti-dsDNA Ab	≦10I U/mL
Anti-RNP Ab	≦5.0 U/mL
Anti-Sm Ab	≦5.0 U/mL
Anti-SS-A/Ro Ab	≦5.0 U/mL
Anti-SS-B/La Ab	≦5.0 U/mL
Anti-Scl 70 Ab	≦5.0 U/mL
Anti-centromere Ab	≦5.0 U/mL
Anti-CL.β2GPI Ab	≦1.3 U/mL
Anti-CALG Ab	≦1.0 U/mL
LAC	≦1.0 U/mL
PR3-ANCA	≦1.0I U/mL
MPO-ANCA	≦1.0 U/mL
RF	≦5.0 U/mL
Anti-CCP Ab	≦0.5 U/mL
Anti-ARS Ab	10 U/mL
Anti-RNA polymerase III Ab	15.2